Question 4161
Topic: 6. SpineWhich of the following congenital spinal anomalies has the highest risk of rapid curve progression and requires the earliest surgical intervention?
Correct Answer & Explanation
. Block vertebra
Practice Set 209 of 379
This practice set contains high-yield board review questions covering key concepts in 6. Spine. Each clinical scenario is designed to test your diagnostic and management skills relevant to this subspecialty.
Which of the following congenital spinal anomalies has the highest risk of rapid curve progression and requires the earliest surgical intervention?
. Block vertebra
A 14-year-old non-ambulatory boy with Duchenne muscular dystrophy develops a progressive neuromuscular scoliosis of 45 degrees. Which of the following is an established principle regarding surgical treatment for this patient?
. Surgery should be delayed until the curve exceeds 90 degrees
A 13-year-old boy with infantile idiopathic scoliosis was treated nonoperatively. Radiographs currently show a 55-degree thoracic curve. Which initial radiographic measurement obtained during infancy was most likely predictive of this curve progression?
. Cobb angle greater than 10 degrees
A 14-year-old female undergoes posterior spinal fusion for adolescent idiopathic scoliosis. Intraoperatively, neuromonitoring demonstrates a sudden, sustained loss of somatosensory evoked potentials (SSEPs) and motor evoked potentials (MEPs) bilaterally during rod derotation. What is the most appropriate immediate first step?
. Administer high-dose methylprednisolone
A 6-month-old infant is diagnosed with an atypical, left-sided thoracic congenital scoliosis curve. A screening renal ultrasound is normal. What other diagnostic study is mandatory to rule out commonly associated anomalies?
. Echocardiogram
Which of the following vertebral anomalies represents the highest risk of curve progression in congenital scoliosis?
. Block vertebra
In a 6-month-old infant with infantile idiopathic scoliosis, a Mehta rib-vertebra angle difference (RVAD) of 25 degrees at the apical vertebra is most highly predictive of which of the following?
. Spontaneous resolution of the curve
A 13-year-old non-ambulatory boy with Duchenne muscular dystrophy develops a progressive 45-degree neuromuscular scoliosis with pelvic obliquity. What is the most appropriate management?
. Observation with serial radiographs
A 12-year-old premenarchal girl (Risser 0) presents with adolescent idiopathic scoliosis. Radiographs demonstrate a progressive right thoracic curve of 52 degrees. What is the most appropriate definitive management?
. Observation with serial radiographs every 6 months
In the initial radiographic evaluation of infantile idiopathic scoliosis, which of the following measurements is the most reliable predictor of curve progression?
. Cobb angle greater than 10 degrees
A 14-year-old boy with Duchenne muscular dystrophy presents with a progressive thoracolumbar scoliosis measuring 45 degrees. His forced vital capacity (FVC) is 45% of predicted. What is the recommended treatment?
. Observation until the curve reaches 60 degrees
A 9-month-old boy presents with an infantile idiopathic scoliosis. Radiographs demonstrate a 30-degree left thoracic curve. The rib-vertebral angle difference (RVAD) is calculated to be 25 degrees. What is the most appropriate management?
. Observation with radiographs every 6 months
A 14-year-old boy with Duchenne muscular dystrophy who is wheelchair-bound develops a 45-degree progressive thoracolumbar scoliosis. His forced vital capacity (FVC) is 40% of predicted. What is the most appropriate management of his spinal deformity?
. Custom-molded TLSO bracing
A 2-year-old child presents with a congenital spinal deformity. Radiographs show multiple vertebral anomalies. Which of the following anomaly patterns is associated with the highest risk of rapid curve progression?
. Block vertebra
During a posterior spinal fusion for adolescent idiopathic scoliosis in a 15-year-old female, the intraoperative neuromonitoring demonstrates a sudden loss of transcranial motor evoked potentials (MEPs) bilaterally, while somatosensory evoked potentials (SSEPs) remain intact. What is the most likely neurologic event?
. Anterior spinal artery ischemia
A 13-year-old gymnast presents with chronic lower back pain. Radiographs reveal an isthmic spondylolisthesis at L5-S1 with 60% forward translation (Meyerding Grade III). She has failed 6 months of physical therapy. What is the most appropriate surgical management?
. Pars interarticularis repair (Buck's procedure)
A 10-year-old boy with neurofibromatosis type 1 (NF-1) develops a 45-degree, sharp, short angular thoracic kyphoscoliosis. Rib penciling and dural ectasia are noted on advanced imaging. What is the recommended surgical management for this patient?

. Posterior spinal fusion alone with pedicle screw construct
A 3-year-old boy presents with a 35-degree right thoracic curve. The rib-vertebral angle difference (RVAD) of Mehta is calculated at 25 degrees on the AP radiograph. What is the most appropriate management for this condition?
. Observation with repeat radiographs in 6 months
A 12-year-old girl presents with a painless scoliotic deformity. Radiographs reveal a 35-degree left-sided thoracic curve. Neurologic examination is unremarkable. What is the most appropriate next step in evaluation?
. CT scan of the thoracic spine
Which of the following congenital spinal anomalies carries the highest risk of scoliotic curve progression and typically requires early surgical intervention?
. Block vertebra