Question 161
Topic: Thoracolumbar Spine & DeformityWhich of the following characterizes Russell-Silver syndrome:
Correct Answer & Explanation
. Hemiatrophy
Practice Set 9 of 49
This practice set contains high-yield board review questions covering key concepts in Thoracolumbar Spine & Deformity. Each clinical scenario is designed to test your diagnostic and management skills relevant to this subspecialty.
Which of the following characterizes Russell-Silver syndrome:
. Hemiatrophy
. Thoracic curves larger than 80°
. A patient younger than 2 years old
For a patient who has thoracic idiopathic scoliosis of the surgical range, the distance between the thecal sac and the apical thoracic pedicle on the concave side is:
. Less than 1 mm
A 1-year-old boy presents with an infantile idiopathic scoliosis curve measuring 30 degrees. Which radiographic measurement is the most reliable prognostic indicator for curve progression?
. Rib-vertebral angle difference (RVAD) of Mehta
A 14-year-old gymnast complains of chronic lower back pain. Radiographs show a grade II spondylolisthesis at L5-S1. What radiographic parameter is most predictive of future slip progression?
. Slip angle (sagittal roll)
In a 6-year-old boy diagnosed with Duchenne Muscular Dystrophy (DMD), the administration of systemic corticosteroids is aimed primarily at achieving which of the following?
. Prolonging independent ambulation
A 25-year-old male sustains a burst fracture of L1 after a fall. He has no neurologic deficits. Which radiographic finding is the strongest indication for operative stabilization rather than non-operative management?
. Disruption of the posterior ligamentous complex (PLC)
A 45-year-old man falls from a height and sustains an L1 burst fracture. His neurological examination is normal. A CT scan demonstrates 30% canal compromise, and MRI confirms an intact posterior ligamentous complex. His Thoracolumbar Injury Classification and Severity (TLICS) score is calculated as 2. What is the most appropriate management?
. Thoracolumbosacral orthosis (TLSO)
. Grade III
A 14-year-old female gymnast complains of mechanical lower back pain for 8 months that limits her sports participation. Lateral lumbar radiographs reveal a bilateral pars interarticularis defect at L5 with a 40% anterior translation of L5 on S1 (Grade II isthmic spondylolisthesis). She has failed 6 months of structured physical therapy. What is the most appropriate surgical treatment?
. L5-S1 in situ posterolateral fusion
. An abnormal neurologic examination
. 20°
The normal values (±2 standard deviations) for kyphosis in the general population of children and adolescents are:
. 20° to 50°
The most common cause of neurologic deficit in patients with Down syndrome is:
. Atlantoaxial instability
. Restrictive lung disease
. Positive family history of scoliosis
A 12-year-old patient has a rigid, 135° scoliosis. Gradually increasing halo- gravity traction is planned in correcting the curve. The maximum weight that should be used is:
. 35% to 45% of body weight
Which of the following is the greatest risk factor for the progression of isthmic spondylolisthesis in a pediatric patient?
. High slip angle (>45 degrees)
Emery-Dreifuss muscular dystrophy is unique among the dystrophies because of the development of which deformity:
. Neck extension contracture