This practice set contains high-yield board review questions covering key concepts in 4. Pediatrics. Each clinical scenario is designed to test your diagnostic and management skills relevant to this subspecialty.
Question 1721
Topic: 4. Pediatrics
According to the Ponseti method for the treatment of idiopathic congenital talipes equinovarus, what is the correct sequential order of deformity correction?
Correct Answer & Explanation
. Cavus, Adductus, Varus, Equinus
Explanation
The mnemonic CAVE dictates the sequential correction of clubfoot deformity in the Ponseti method: Cavus (corrected by elevating the first ray), Adductus, Varus, and finally Equinus (which often requires a percutaneous Achilles tenotomy).
Question 1722
Topic: Pediatric Upper Extremity & Spine
A 6-year-old boy falls from monkey bars and sustains an extension-type supracondylar humerus fracture. Radiographs show a Gartland Type III pattern with posteromedial displacement of the distal fragment. Which peripheral nerve is at the greatest risk of injury in this specific displacement pattern?
Correct Answer & Explanation
. Radial nerve
Explanation
Posteromedial displacement of the distal fragment causes the proximal metaphyseal fragment to spike anterolaterally, placing the radial nerve at the highest risk of injury. Posterolateral displacement endangers the median nerve (or AIN).
Question 1723
Topic: 4. Pediatrics
A 19-year-old male sustains a posterior sternoclavicular dislocation during a rugby match. The orthopedic surgeon plans an open reduction. During preoperative planning, the surgeon recalls that the medial clavicle physis is typically the last primary ossification center to fuse in the human body. This may mean the injury is a physeal fracture rather than a true dislocation. At what age does the medial clavicular physis typically fuse?
Correct Answer & Explanation
. 23 to 25 years
Explanation
The medial clavicle physis is the last growth plate in the body to fuse. Ossification begins around age 18, and complete fusion does not occur until 23 to 25 years of age. Therefore, apparent sternoclavicular dislocations in patients under 25 are frequently Salter-Harris physeal fractures.
Question 1724
Topic: Pediatric Lower Extremity
During the Ponseti method for treating idiopathic clubfoot, a specific sequence of deformity correction must be strictly followed. Which of the following components of the deformity is corrected last?
Correct Answer & Explanation
. Ankle equinus
Explanation
The Ponseti method corrects clubfoot in the sequence of CAVE: Cavus, Adductus, Varus, and finally Equinus. Equinus is addressed last, often requiring a percutaneous Achilles tenotomy.
Question 1725
Topic: Pediatric Lower Extremity
A 55-year-old woman presents with chronic, insidious midfoot pain and a progressive flatfoot. Radiographs demonstrate a comma-shaped deformity of the tarsal navicular with lateral subluxation of the talar head and dorsal fragmentation. What is the most likely diagnosis?
Correct Answer & Explanation
. Müller-Weiss disease
Explanation
Müller-Weiss disease is spontaneous osteonecrosis of the tarsal navicular in adults, presenting with midfoot pain, a characteristic comma-shaped navicular, and lateral talar subluxation. Köhler disease is navicular osteonecrosis but occurs in young children.
Question 1726
Topic: 4. Pediatrics
A 12-year-old boy who has had a 1-month history of right thigh pain and a limp reports worsening of the pain after a fall, and he can no longer walk or bear weight on the involved extremity. Radiographs of the pelvis reveal a slipped capital femoral epiphysis with moderate to severe displacement. While positioning the patient on the fracture table for screw fixation, partial reduction of the slip is achieved. No further reduction maneuvers are attempted, and the epiphysis is stabilized with a single cannulated screw. What complication is most likely to develop following this procedure?
Correct Answer & Explanation
. Osteonecrosis
Explanation
This is an unstable slipped capital femoral epiphysis. Reduction of an unstable slip often occurs unintentionally with induction of anesthesia and positioning of the patient for surgery. The rate of satisfactory results is lower primarily because of a much higher incidence of osteonecrosis following internal fixation of an unstable slip.
Question 1727
Topic: 4. Pediatrics
A 6-year-old boy sustains a Gartland type III supracondylar humerus fracture. Upon arrival, his hand is pale and pulseless. He is immediately taken to the operating room, where closed reduction and percutaneous pinning are successfully performed. Following fixation, the hand becomes warm and pink with a capillary refill time of less than 2 seconds, but the radial pulse remains absent on palpation and Doppler ultrasound. What is the most appropriate next step in management?
Correct Answer & Explanation
. Observation and inpatient admission with serial vascular checks
Explanation
The 'pink, pulseless hand' following reduction and pinning of a pediatric supracondylar humerus fracture is a well-known clinical scenario. Current pediatric orthopaedic consensus and AAOS guidelines strongly recommend observation as long as the hand is well-perfused (warm, pink, capillary refill <2 seconds). Collateral circulation is robust in children, and the radial pulse often returns within days to weeks as vasospasm resolves. Emergent vascular exploration is reserved for hands that remain cold, white, and poorly perfused after reduction.
Question 1728
Topic: 4. Pediatrics
A 5-year-old child sustains a Gartland type III supracondylar humerus fracture. The hand is pink but lacks a palpable radial pulse. Following closed reduction and percutaneous pinning, the hand remains well-perfused (pink) with brisk capillary refill, but the radial pulse remains absent. What is the next best step in management?
Correct Answer & Explanation
. Observation and hospital admission for close clinical monitoring
Explanation
For a 'pink, pulseless' hand following stable reduction and pinning of a pediatric supracondylar humerus fracture, current guidelines recommend observation and close clinical monitoring. The collateral circulation around the elbow is typically sufficient to maintain viability.
Question 1729
Topic: 4. Pediatrics
A 6-year-old boy presents with a completely displaced, extension-type supracondylar humerus fracture. His hand is pink and warm, but the radial pulse is absent. After closed reduction and percutaneous pinning, the hand remains well-perfused with excellent capillary refill, but the radial pulse is still non-palpable. What is the next most appropriate step in management?
Correct Answer & Explanation
. Close clinical observation and admission for 24-48 hours
Explanation
In a 'pulseless, pink' hand following an adequate and stable reduction of a pediatric supracondylar humerus fracture, the standard of care is close clinical observation. Collateral circulation is sufficient to maintain viability, and the pulse typically returns within a few days to weeks.
Question 1730
Topic: 4. Pediatrics
A 6-year-old boy presents with a displaced extension-type supracondylar humerus fracture. On initial examination, the hand is pink and well-perfused, but the radial pulse is absent. After closed reduction and percutaneous pinning, the radial pulse remains absent, but the hand remains pink with a capillary refill time of less than 2 seconds. What is the most appropriate next step in management?
Correct Answer & Explanation
. Admit for close observation and neurovascular checks
Explanation
A 'pink, pulseless' hand following reduction and pinning of a pediatric supracondylar humerus fracture is indicative of adequate collateral circulation despite probable brachial artery spasm, kinking, or entrapment. Current AAOS and POSNA guidelines recommend admission for close observation (typically 24-48 hours) as long as the hand remains well-perfused (warm, pink, capillary refill <2 seconds). Immediate exploration is reserved for a 'white, pulseless' hand (dysvascular) that does not improve after reduction.
Question 1731
Topic: 4. Pediatrics
A 2-year-old child presents with bilateral genu varum. Standing radiographs demonstrate a metaphyseal-diaphyseal angle (MDA) of 20 degrees bilaterally. What is the most appropriate initial management?
Correct Answer & Explanation
. Bilateral knee-ankle-foot orthoses (KAFOs)
Explanation
In a child under 3 years old with suspected infantile Blount's disease, a metaphyseal-diaphyseal angle (MDA or Drennan's angle) greater than 16 degrees strongly suggests true Blount's disease rather than physiologic bowing. The initial treatment for infantile Blount's disease in children under age 3 is bracing with knee-ankle-foot orthoses (KAFOs). Surgery is indicated if bracing fails or if the child presents at an older age with advanced Langenskiöld stages.
Question 1732
Topic: 4. Pediatrics
A 9-year-old girl undergoes tension band plating (guided growth) for idiopathic genu valgum. Following clinical and radiographic correction of the mechanical axis, the plates and screws are removed. She returns to the clinic 18 months later with recurrent genu valgum. What is the most likely cause of this recurrent deformity?
Correct Answer & Explanation
. Rebound phenomenon due to rapid periosteal growth
Explanation
The 'rebound phenomenon' is a well-documented complication following implant removal in guided growth (tension band plating), particularly in younger patients with significant remaining growth potential. The physis 'rebounds' and grows at an accelerated rate, causing a recurrence of the original deformity. Some surgeons intentionally overcorrect by a few degrees to account for this expected rebound.
Question 1733
Topic: 4. Pediatrics
A 30-month-old child presents with bilateral symmetric genu varum. Radiographs reveal a metaphyseal-diaphyseal angle of 18 degrees and lateral thrust during ambulation. Which of the following is the most appropriate initial management?
Correct Answer & Explanation
. Knee-ankle-foot orthosis (KAFO)
Explanation
A metaphyseal-diaphyseal angle greater than 16 degrees strongly suggests infantile Blount's disease rather than physiologic bowing. In children under 3 years old with Langenskiöld stage I or II, full-time bracing with a KAFO is the recommended initial management.
Question 1734
Topic: 4. Pediatrics
Which of the following radiographic or clinical parameters is uniquely essential for programming a hexapod circular external fixator (e.g., Taylor Spatial Frame) but is not explicitly required for building a standard Ilizarov frame?
Correct Answer & Explanation
. The mounting parameters (e.g., distance from the reference ring to the origin)
Explanation
Hexapod fixators utilize computer software to generate a prescription for 6-axis deformity correction. This requires precise mounting parameters, which describe the spatial relationship between the reference ring and the reference bone segment.
Question 1735
Topic: 4. Pediatrics
An 8-year-old severely obese male presents with worsening unilateral tibia vara. Radiographs reveal a depressed medial tibial plateau, profound metaphyseal beaking, and an established physeal bar (Langenskiöld stage VI). What is the most definitive surgical management?
Correct Answer & Explanation
. Physeal bar excision, medial plateau elevation, and corrective osteotomy
Explanation
In advanced infantile Blount disease (Langenskiöld stage V-VI), a bony bar crosses the physis and causes intra-articular depression. Treatment requires resection of the physeal bar, elevation of the depressed medial plateau, and a proximal tibial osteotomy to restore mechanical alignment.
Question 1736
Topic: 4. Pediatrics
When utilizing the principles of distraction osteogenesis (Ilizarov method) for a tibial lengthening procedure in a healthy adult, what is the optimal latency period and rate of distraction to ensure ideal regenerate bone formation?
Correct Answer & Explanation
. 7-10 days latency; 1.0 mm/day
Explanation
Ilizarov established that a latency period of 7-10 days allows for early callus formation before distraction begins. The ideal distraction rate is 1.0 mm per day (typically divided into 0.25 mm increments four times daily) to prevent premature consolidation or poor regenerate formation.
Question 1737
Topic: Pediatric Hip
A 12-year-old obese male presents with a stable slipped capital femoral epiphysis (SCFE) of the left hip. The surgeon recommends in situ pinning of the left hip. What is the most widely accepted absolute indication for prophylactic in situ pinning of the asymptomatic, contralateral right hip?
Correct Answer & Explanation
. Presence of an underlying endocrine disorder (e.g., hypothyroidism)
Explanation
Prophylactic pinning of the contralateral hip in SCFE is universally recommended for patients with underlying endocrine disorders (such as hypothyroidism, panhypopituitarism, or renal osteodystrophy) or prior pelvic radiation, as their risk of developing a contralateral slip is exceedingly high (up to 100%).
Question 1738
Topic: 4. Pediatrics
A 2-year-old child presents with bilateral absent thumbs and marked radial shortening. Laboratory tests reveal pancytopenia. Chromosomal breakage testing with diepoxybutane (DEB) is strongly positive. What is the inheritance pattern and primary cellular defect associated with this condition?
Correct Answer & Explanation
. Autosomal recessive; defect in DNA interstrand cross-link repair
Explanation
The patient has Fanconi anemia, which typically presents with radial longitudinal deficiency (absent thumb/radius) and aplastic anemia (pancytopenia). It is inherited in an autosomal recessive pattern and is characterized by a failure in DNA interstrand cross-link repair. Diagnosis is confirmed by increased chromosomal breakage after exposure to clastogenic agents like DEB.
Question 1739
Topic: 4. Pediatrics
A 4-month-old infant is noted to have a hairy patch and a sacral dimple above the gluteal crease. MRI confirms a thickened filum terminale and a conus medullaris terminating at the L4 level. What is the specific embryological defect primarily responsible for this tethered cord syndrome?
Correct Answer & Explanation
. Failure of secondary neurulation and retrogressive differentiation
Explanation
The development of the lower sacral and coccygeal segments of the spinal cord occurs via secondary neurulation. During the subsequent phase of retrogressive differentiation, the terminal portion of the neural tube undergoes atrophy to form the filum terminale, allowing the conus medullaris to ascend. Failure of this process leads to a thickened filum terminale and a low-lying, tethered conus medullaris. Primary neurulation defects result in open defects like myelomeningocele.
Question 1740
Topic: Pediatric Upper Extremity & Spine
According to the Lenke classification for adolescent idiopathic scoliosis, a curve is considered structurally significant and should be included in the fusion construct if the Cobb angle fails to reduce below what threshold on side-bending radiographs?
Correct Answer & Explanation
. 25 degrees
Explanation
In the Lenke classification system, a minor curve is considered structural if it does not bend down to less than 25 degrees on lateral side-bending radiographs. Structural curves must be included in the final fusion construct to maintain overall coronal balance.
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