This practice set contains high-yield board review questions covering key concepts in 4. Pediatrics. Each clinical scenario is designed to test your diagnostic and management skills relevant to this subspecialty.
Question 821
Topic: Pediatric Hip
A 12-year-old obese boy presents with a 3-week history of groin pain and a limp. Examination reveals obligatory external rotation with hip flexion. Radiographs confirm a stable slipped capital femoral epiphysis (SCFE). What is the most appropriate standard surgical management?
Correct Answer & Explanation
. In situ pinning with a single cannulated screw
Explanation
The gold standard treatment for a stable SCFE is in situ percutaneous pinning using a single partially threaded cannulated screw. This prevents further slippage while minimizing the risk of avascular necrosis and chondrolysis.
Question 822
Topic: Pediatric Upper Extremity & Spine
A 6-year-old boy falls off monkey bars and sustains a significantly displaced supracondylar humerus fracture (Gartland Type III). He has an absent radial pulse but a well-perfused, "pink, and warm" hand. What is the most appropriate initial management in the operating room?
Correct Answer & Explanation
. Closed reduction and percutaneous pinning followed by reassessment of the pulse
Explanation
For a "pink, pulseless" hand in the setting of a displaced supracondylar humerus fracture, the initial step is urgent closed reduction and percutaneous pinning. The pulse frequently returns after fracture realignment; vascular exploration is reserved for cases where the hand remains dysvascular (white and pulseless) after reduction.
Question 823
Topic: 4. Pediatrics
All of the following may be present in a child with type IIIA hypoplasia except:
Correct Answer & Explanation
. Unstable carpometacarpal (CMC) joint
Explanation
Type IIIA hypoplasia includes web space narrowing, thenar atrophy, MP joint laxity, and extrinsic tendon abnormalities. Type IIIA is distinguished from a type IIIB by the fact that a stable CMC joint exists. Because a stable CMC joint exists, a reconstruction is the treatment of choice. When the CMC joint is unstable, as in type IIIB hypoplasia, a pollicization is necessary to restore thumb stability.
Question 824
Topic: Pediatric Hip
A 13-year-old obese boy presents with an insidious onset of knee pain and a limp. A pelvic radiograph is obtained.
Which of the following radiographic lines is most appropriate to evaluate for Slipped Capital Femoral Epiphysis (SCFE)?
Correct Answer & Explanation
. Klein's line
Explanation
Klein's line is drawn along the superior margin of the femoral neck on an AP and frog-leg lateral radiograph. In a normal hip, it intersects the lateral portion of the femoral epiphysis; in SCFE, the epiphysis falls below this line.
Question 825
Topic: 4. Pediatrics
A 4-month-old infant is being treated with a Pavlik harness for Developmental Dysplasia of the Hip (DDH). The mother notes that the child has stopped kicking the affected leg. On exam, the child lacks active knee extension. Which nerve is most likely compressed due to hyperflexion?
Correct Answer & Explanation
. Femoral nerve
Explanation
Femoral nerve palsy is a known complication of Pavlik harness treatment when the hip is placed in excessive flexion. The harness should be temporarily discontinued, and function almost always recovers spontaneously.
Question 826
Topic: Pediatric Hip
An obese 13-year-old boy presents with left knee pain and an obligate external rotation of the hip during flexion. The radiograph is shown below.
When treating this condition with in situ percutaneous pinning, what is the most significant iatrogenic risk factor for the development of chondrolysis?
In Slipped Capital Femoral Epiphysis (SCFE), unrecognized intra-articular screw penetration is a major risk factor for chondrolysis. Surgeons must use the "approach-withdraw" fluoroscopic technique to confirm the screw tip is entirely within the femoral head.
Question 827
Topic: Pediatric Hip
A 6-month-old infant with developmental dysplasia of the hip (DDH) failed Pavlik harness treatment and is scheduled for a closed reduction and spica casting. During the procedure, the surgeon assesses the "safe zone" of Ramsey. How is this zone defined?
Correct Answer & Explanation
. The arc of motion between maximum abduction and the angle of re-dislocation in adduction
Explanation
Ramsey's safe zone is the arc of motion between maximum abduction (limited by the adductors) and the angle at which the hip re-dislocates as it is adducted. Immobilization within this zone prevents both avascular necrosis (from excessive abduction) and re-dislocation.
Question 828
Topic: 4. Pediatrics
Congenital thumb duplication:
Correct Answer & Explanation
. Often presents with a hypoplastic radial thumb and a dominant-appearing ulnar thumb
Explanation
Experts recommend treating congenital thumb duplication before the age of 6 months, when the potential for growth and remodeling is greatest. The condition usually presents unilaterally, lacking association with other systemic abnormalities, and usually presents with a hypoplastic radial duplicate and dominant ulnar duplicate.
Question 829
Topic: 4. Pediatrics
One of the more common complications of congenital thumb duplication reconstruction is:
Correct Answer & Explanation
. Ulnar deviation at metacarpophalangeal joint and radial deviation at interphalangeal joint
Explanation
A Z-deformity, with ulnar deviation at the MC P joint and radial deviation at the IP joint, is one of the most common complications after reconstruction. Weakness, paresthesias, and wound complications are uncommon possible complications.
Question 830
Topic: 4. Pediatrics
A 6-year-old child sustains an extension-type supracondylar fracture of the humerus. On examination, the child is unable to form an "A-OK" sign with the thumb and index finger. Which nerve is most likely injured?
Correct Answer & Explanation
. Anterior interosseous nerve (AIN)
Explanation
The anterior interosseous nerve (AIN) is the most commonly injured nerve in extension-type pediatric supracondylar humerus fractures. Injury to the AIN results in weakness of the flexor pollicis longus and flexor digitorum profundus to the index finger, preventing the "A-OK" sign.
Question 831
Topic: 4. Pediatrics
A 4-month-old infant is treated with a Pavlik harness for developmental dysplasia of the hip. At the 2-week follow-up, the infant is noted to have decreased active knee extension on the affected side. What is the most appropriate next step in management?
Correct Answer & Explanation
. Discontinue the harness immediately
Explanation
Decreased active knee extension indicates a femoral nerve palsy, a known complication of Pavlik harness treatment due to excessive hip flexion. The harness must be discontinued immediately to allow the nerve to recover before attempting alternative treatments.
Question 832
Topic: Pediatric Hip
A 13-year-old obese male presents with a 3-week history of right groin pain and a slight limp. On physical examination, as the right hip is passively flexed, it obligatorily deviates into external rotation. What is the eponymous name of this clinical sign?
Correct Answer & Explanation
. Drehmann sign
Explanation
The Drehmann sign is the obligatory external rotation of the hip during passive flexion. It is a classic and highly indicative physical examination finding in patients with a slipped capital femoral epiphysis (SCFE).
Question 833
Topic: 4. Pediatrics
A 6-year-old child sustains a severely displaced extension-type supracondylar humerus fracture. On presentation, the hand is pink but the radial pulse is absent. Following urgent closed reduction and percutaneous pinning, the hand remains pink with brisk capillary refill, but the radial pulse is still not palpable. What is the most appropriate next step?
Correct Answer & Explanation
. Observation and admission for 24-48 hours
Explanation
A 'pulseless but pink' hand after reduction and pinning of a pediatric supracondylar humerus fracture indicates adequate collateral perfusion. The standard of care is close observation for 24-48 hours, as the pulse often returns once spasm and edema subside.
Question 834
Topic: Pediatric Upper Extremity & Spine
Which of the following is not usually associated with radial deficiency:
Correct Answer & Explanation
. Larsen syndrome
Explanation
Patients with thrombocytopenia absent radii, Fanconi anemia, Holt-Oram syndrome, and cardiac anomolies all are associated with radial deficiency. Larsen syndrome is associated with multiple, larger joint dislocation.
Question 835
Topic: 4. Pediatrics
A 6-year-old boy presents with a Salter-Harris II distal radius fracture 3 weeks after injury. He is nontender and neurologically intact. On radiographs, he has a 35ยฐ dorsal angulation. The appropriate course of treatment is:
Correct Answer & Explanation
. Observe, cast, follow with serial radiographs for at least 2 years
Explanation
For a patient with delayed presentation of a distal radius fracture, appropriate management includes casting and observation for at least 2 years to assess physeal damage and remodeling. The patient may require osteotomy if remodeling does not occur.
Question 836
Topic: 4. Pediatrics
A 24-year-old man presents with a short forearm and a hand deformity. The patient is otherwise healthy with no other congenital defects. The clinical appearance of his forearm is shown (Slide). Your diagnosis is:
Correct Answer & Explanation
. Preaxial longitudinal deficiency
Explanation
This is a classic appearance of a radial club hand, which is often referred to as preaxial longitudinal deficiency. Ulnar club hand and postaxial longitudinal deficiency are synonymous.
Question 837
Topic: 4. Pediatrics
A 24-year-old man presents with a short forearm and a hand deformity. The patient is otherwise healthy with no other congenital defects. The clinical appearance of his forearm is shown (Slide). The patient has an elbow flexion contracture of 70ยฐ and desires lengthening. Which of the following statements is not true regarding lengthening:
Correct Answer & Explanation
. Nerve palsies may occur during lengthening.
Explanation
In most cases of radial club hand, excluding a hypoplastic radius, full correction cannot be achieved.
Question 838
Topic: 4. Pediatrics
A 24-year-old man presents with a short forearm and a hand deformity. The patient is otherwise healthy with no other congenital defects. The clinical appearance of his forearm is shown (Slide). Although the patient has a thumb, it is in an abnormal position. Any attempt to make his thumb more functional will be influenced by:
Correct Answer & Explanation
. Presence of a side-to-side finger grip
Explanation
The pattern of usage of the hand is established in the brain by 2 to 3 years of age. Although pollicization has been performed in adolescents, patients continue to prefer a scissor pinch. At 24 years of age, this pattern will be well established. The patient can be coaxed to use his thumb, but it will not be involuntary and automatic.C orrect Answer: Presence of a side-to-side finger grip
Question 839
Topic: Pediatric Upper Extremity & Spine
A radial club hand is the result of an insult during which phase of the gestation period:
Correct Answer & Explanation
. Weeks 4 to 7
Explanation
A radial club hand is the result of an insult during weeks 4 to 7 of gestation.
Question 840
Topic: Pediatric Upper Extremity & Spine
A 15-day-old boy presents with deformity of the right hand. The boy was delivered prematurely and underwent an urgent arterial switch for transposition of great vessels. The patient is in stable condition. He has a radial club hand, and because the radial head cannot be palpated, total absence of radius is suspected. The thumb is absent and the index finger has camptodactyly. The forearm is short compared to the left side, and the patient flexes his elbow upon stimulation. Spontaneous finger motion is also present. A thorough physical examination is performed and a set of investigations is ordered. The results are as follows: complete blood count 10,000/ยตL; platelet 254ร10^3/ยตL; neutrophils 50%; Hb 14.2 g/dL; lymphocytes 40%; Hct 45%; and monocytes 10%. No renal abnormalities were noted on ultrasonogram of the abdomen. A radiograph of the spine is normal. Diagnosis is:
Correct Answer & Explanation
. Holt-Oram syndrome
Explanation
The patient has a radial club hand with a cardiac defect. Because the spine radiograph is normal, the diagnosis cannot be VATER or VACTERL anomaly as both involve vertebrae. Blood work up is normal, making this diagnosis Holt-Oram syndrome.
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