This practice set contains high-yield board review questions covering key concepts in 4. Pediatrics. Each clinical scenario is designed to test your diagnostic and management skills relevant to this subspecialty.
Question 5461
Topic: Pediatric Hip
A 4-month-old female with developmental dysplasia of the hip (DDH) is being treated with a Pavlik harness. During a follow-up, she exhibits decreased active knee extension on the affected side. What is the most likely cause?
Correct Answer & Explanation
. Femoral nerve palsy from excessive hyperflexion
Explanation
Femoral nerve palsy is a known complication of the Pavlik harness, typically caused by excessive hip hyperflexion that compresses the nerve. It presents as decreased active knee extension.
Question 5462
Topic: Pediatric Hip
An obese 13-year-old boy presents with an inability to bear weight on his right leg after a minor fall. Radiographs confirm an acute, unstable slipped capital femoral epiphysis (SCFE). If the surgeon attempts a forceful, anatomic closed reduction prior to internal fixation, the patient is at highest risk for which of the following complications?
Correct Answer & Explanation
. Avascular necrosis (AVN)
Explanation
Forceful or anatomic reduction of an unstable SCFE dramatically increases the risk of avascular necrosis. This occurs due to disruption or tensioning of the fragile posterior retinacular blood supply to the femoral head.
Question 5463
Topic: Pediatric Hip
A 6-week-old female infant undergoes a screening ultrasound of the hip due to a family history of developmental dysplasia of the hip (DDH). The sonographer reports an alpha angle of 50 degrees. According to the Graf classification, what does this alpha angle represent?
Correct Answer & Explanation
. Dysplastic acetabular bony roof
Explanation
In the Graf ultrasound evaluation for DDH, the alpha angle measures the concavity of the bony acetabular roof. An alpha angle less than 60 degrees (such as 50 degrees) indicates a dysplastic or shallow bony roof, typically classifying as a Graf Type II hip.
Question 5464
Topic: 4. Pediatrics
A pediatric orthopedic surgeon initiates treatment for a 2-week-old infant with an idiopathic clubfoot (talipes equinovarus) using the Ponseti casting method. Which of the following represents the correct sequential order of deformity correction?
Correct Answer & Explanation
. Cavus, Adductus, Varus, Equinus
Explanation
The Ponseti method requires sequential correction of the clubfoot deformities following the CAVE mnemonic: Cavus (corrected first by elevating the first ray), Adductus, Varus, and finally Equinus (which often requires a percutaneous Achilles tenotomy).
Question 5465
Topic: Pediatric Upper Extremity & Spine
A 6-year-old boy presents to the emergency department following a fall from monkey bars. Radiographs reveal an extension-type Gartland III supracondylar humerus fracture. After closed reduction and percutaneous pinning, the patient's radial pulse is absent, but the hand is pink, warm, and has a capillary refill time of less than 2 seconds. What is the most appropriate next step in management?
Correct Answer & Explanation
. Observation with close neurovascular monitoring
Explanation
A pulseless, pink, and well-perfused hand following reduction and pinning of a supracondylar humerus fracture should be observed, as collateral circulation is adequate. Arterial exploration is strictly indicated only if the hand is pulseless, pale, and poorly perfused (ischemic) after reduction.
Question 5466
Topic: Pediatric Hip
A 13-year-old obese male presents with a 3-week history of right-sided groin pain and an antalgic gait. Physical examination reveals an obligatory external rotation of the right hip during passive hip flexion. Radiographs confirm a mild, stable slipped capital femoral epiphysis (SCFE). What is the most appropriate definitive management?
Correct Answer & Explanation
. In situ single screw fixation
Explanation
The gold standard treatment for a stable slipped capital femoral epiphysis (SCFE) is in situ fixation using a single partially threaded cannulated screw. Attempting a closed reduction is contraindicated as it severely increases the risk of avascular necrosis of the femoral head.
Question 5467
Topic: 4. Pediatrics
A 24-year-old male presents with recurrent fractures and a 'bone-in-bone' appearance on radiographs. His condition is caused by a failure of osteoclasts to resorb bone. Which of the following mutations is most commonly responsible for the autosomal dominant form of this disease?
Correct Answer & Explanation
. CLCN7
Explanation
Autosomal dominant osteopetrosis (Albers-Schönberg disease) is most commonly caused by a mutation in the CLCN7 gene, which encodes a chloride channel necessary for acidifying the resorption pit. TCIRG1 causes the severe autosomal recessive form. COL1A1 causes Osteogenesis Imperfecta. FGFR3 causes achondroplasia. RUNX2 is associated with cleidocranial dysplasia.
Question 5468
Topic: Pediatric Hip
A 12-year-old obese male presents with left groin pain and an obligatory external rotation of the hip during active flexion. Radiographs show a posterior and inferior displacement of the proximal femoral epiphysis. Which of the following is the strongest indication for prophylactic in situ pinning of the contralateral asymptomatic hip?
Correct Answer & Explanation
. Endocrine disorder (e.g., hypothyroidism)
Explanation
Prophylactic pinning of the contralateral hip in Slipped Capital Femoral Epiphysis (SCFE) is highly recommended in patients with endocrine disorders (such as hypothyroidism, renal osteodystrophy, or growth hormone deficiency) and in children presenting at a very young age (< 10 years), due to the high risk of bilateral involvement.
Question 5469
Topic: 4. Pediatrics
A 4-year-old child presents with rhizomelic short stature, frontal bossing, and midface hypoplasia. Radiographs show narrowing of the interpedicular distances in the lumbar spine and 'champagne glass' pelvis. The genetic mutation responsible for this condition causes an abnormality in which zone of the physis?
Correct Answer & Explanation
. Proliferative zone
Explanation
Achondroplasia is caused by an activating mutation in the FGFR3 gene, which inhibits chondrocyte proliferation. This directly affects the proliferative zone of the physis, leading to defective endochondral ossification.
Question 5470
Topic: Pediatric Hip
A 13-year-old obese male presents with a stable slipped capital femoral epiphysis (SCFE) of the left hip. Prophylactic pinning of the contralateral, asymptomatic hip is most strongly recommended for patients with which of the following underlying conditions?
Correct Answer & Explanation
. Endocrine disorders (e.g., hypothyroidism or panhypopituitarism)
Explanation
Prophylactic pinning of the contralateral hip in SCFE is controversial for typical patients but is highly recommended in patients with an underlying endocrinopathy (e.g., hypothyroidism, renal osteodystrophy, growth hormone deficiency), as their risk for a contralateral slip approaches 50-100%.
Question 5471
Topic: Pediatric Lower Extremity
The Ponseti method is the gold standard for the conservative management of idiopathic clubfoot (talipes equinovarus). What is the correct sequence of deformity correction during serial casting?
Correct Answer & Explanation
. Cavus, Adductus, Varus, Equinus
Explanation
The Ponseti method requires sequential correction of the clubfoot deformities using the mnemonic CAVE: first Cavus (by elevating the first ray to supinate the forefoot), then Adductus, then Varus, and finally Equinus (which often requires a percutaneous Achilles tenotomy).
Question 5472
Topic: Pediatric Hip
A 3-month-old infant is being treated with a Pavlik harness for Developmental Dysplasia of the Hip (DDH). At follow-up, the parents report the infant is not kicking the affected leg. Physical exam reveals absent active knee extension, but active ankle dorsiflexion is intact. Which complication of the harness has most likely occurred?
Correct Answer & Explanation
. Femoral nerve palsy
Explanation
Hyperflexion of the hips in a Pavlik harness can compress the femoral nerve against the rim of the pelvis or inguinal ligament, leading to a femoral nerve palsy. This manifests clinically as an inability to actively extend the knee. The treatment is temporary discontinuation or adjustment of the harness.
Question 5473
Topic: Pediatric Hip
A 4-week-old female infant is diagnosed with developmental dysplasia of the hip (DDH) and placed in a Pavlik harness. While monitoring the patient, what is the most common neurological complication resulting from excessive hip flexion in this device?
Correct Answer & Explanation
. Femoral nerve palsy
Explanation
Excessive hip flexion in a Pavlik harness can cause impingement leading to a femoral nerve palsy. This typically presents as a loss of active knee extension. Conversely, excessive abduction in the harness places the patient at high risk for avascular necrosis (AVN) of the femoral head.
Question 5474
Topic: Pediatric Hip
A 12-year-old overweight boy presents with left knee pain and a limp. Examination reveals obligate external rotation of the left hip during passive hip flexion. Radiographs confirm a slipped capital femoral epiphysis (SCFE). Which of the following is the typical direction of the epiphyseal displacement relative to the femoral neck?
Correct Answer & Explanation
. Posterior and inferior
Explanation
In a slipped capital femoral epiphysis (SCFE), the femoral epiphysis typically displaces posteriorly and inferiorly relative to the femoral neck. Conversely, the metaphysis (femoral neck) translates anteriorly and superiorly.
Question 5475
Topic: Pediatric Upper Extremity & Spine
A 6-year-old boy presents with a Gartland type III supracondylar humerus fracture. The hand is pink but pulseless. After closed reduction and percutaneous pinning, the hand remains pink and pulseless. What is the most appropriate next step?
Correct Answer & Explanation
. Observation and hospital admission
Explanation
A "pink, pulseless" hand after successful reduction and pinning of a supracondylar fracture usually signifies adequate collateral circulation. Observation is indicated, as the palpable radial pulse often returns within 24-48 hours.
Question 5476
Topic: Pediatric Hip
A 6-week-old female is treated with a Pavlik harness for developmental dysplasia of the hip. At the one-week follow-up, she exhibits decreased active knee extension on the treated side. What is the most likely cause?
Correct Answer & Explanation
. Hyperflexion of the hip in the harness
Explanation
Hyperflexion of the hip in a Pavlik harness can compress the femoral nerve against the inguinal ligament, leading to a transient femoral nerve palsy. This manifests clinically as decreased active knee extension.
Question 5477
Topic: Pediatric Hip
A 14-year-old boy is diagnosed with an unstable slipped capital femoral epiphysis (SCFE). Which of the following describes the most critical consequence differentiating an unstable SCFE from a stable SCFE?
Correct Answer & Explanation
. Higher risk of avascular necrosis (AVN)
Explanation
The Loder classification distinguishes stable from unstable SCFE based on the ability to bear weight. Unstable slips carry a drastically higher risk of avascular necrosis (up to 50%), dictating urgency and care in surgical management.
Question 5478
Topic: Pediatric Hip
A 3-month-old infant is currently being treated with a Pavlik harness for developmental dysplasia of the hip (DDH). At the routine weekly follow-up, the infant is noted to have an absence of active knee extension on the treated side. What is the most likely cause of this physical finding?
Correct Answer & Explanation
. Femoral nerve palsy from excessive flexion
Explanation
Femoral nerve palsy is a known complication of Pavlik harness treatment, usually caused by excessive hip flexion (typically >120 degrees). It presents as decreased or absent active knee extension. The harness must be adjusted to reduce flexion or temporarily discontinued if the palsy persists. Excessive abduction in a Pavlik harness is associated with an increased risk of avascular necrosis (AVN) of the femoral head.
Question 5479
Topic: Pediatric Hip
Which of the following clinical scenarios serves as the strongest indication for prophylactic in situ pinning of the contralateral asymptomatic hip in a patient who presents with a unilateral slipped capital femoral epiphysis (SCFE)?
Correct Answer & Explanation
. Presence of an endocrine disorder such as hypothyroidism
Explanation
Prophylactic pinning of the contralateral hip in unilateral SCFE is highly recommended in patients with specific risk factors that predispose them to bilateral involvement. The strongest indications include an underlying endocrine disorder (e.g., hypothyroidism, panhypopituitarism, renal osteodystrophy), previous pelvic radiation, and very young age at presentation (typically < 10 years for boys and < 9 for girls). Endocrine disorders carry an extremely high risk of bilateral SCFE, justifying prophylactic fixation.
Question 5480
Topic: Pediatric Hip
Prophylactic in situ pinning of the asymptomatic contralateral hip in a patient with a slipped capital femoral epiphysis (SCFE) is most strongly indicated in a patient with which of the following underlying conditions?
Correct Answer & Explanation
. Renal osteodystrophy
Explanation
Prophylactic pinning of the contralateral hip in SCFE is indicated for patients with a high risk of subsequent bilateral slip. Endocrine and metabolic disorders, such as renal osteodystrophy, hypothyroidism, and prior pelvic radiation, are strong indications for prophylactic fixation due to the high incidence of bilaterality.
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