This practice set contains high-yield board review questions covering key concepts in 4. Pediatrics. Each clinical scenario is designed to test your diagnostic and management skills relevant to this subspecialty.
Question 4601
Topic: Pediatric Hip
A 12-year-old boy with a BMI of 32 presents with a left slipped capital femoral epiphysis (SCFE). Prophylactic pinning of the contralateral asymptomatic hip is most strongly indicated in which of the following scenarios?
Correct Answer & Explanation
. The patient is an African American male
Explanation
Prophylactic pinning of the contralateral hip in SCFE is controversial for idiopathic cases but is strongly indicated in patients with underlying endocrinopathies or metabolic bone diseases (e.g., renal osteodystrophy, hypothyroidism, panhypopituitarism) and in patients receiving radiation therapy, because the risk of contralateral slip approaches 50-100% in these populations.
Question 4602
Topic: Pediatric Lower Extremity
When applying the Ponseti method for the correction of a severe idiopathic clubfoot, which of the following represents the correct sequential order of deformity correction?
Correct Answer & Explanation
. Cavus, Adductus, Varus, Equinus
Explanation
The Ponseti method corrects clubfoot deformities in a specific sequence summarized by the acronym CAVE: Cavus, Adductus, Varus, and Equinus. The cavus is corrected first by elevating the first ray. The adductus and varus are then corrected simultaneously by abducting the foot around the head of the talus. Equinus is corrected last, often requiring a percutaneous Achilles tenotomy.
Question 4603
Topic: 4. Pediatrics
A 7-year-old with spastic quadriplegic cerebral palsy has progressive hip subluxation with a Reimer's migration index of 45%. The primary deforming forces responsible for this progressive subluxation are spasticity of which muscle groups?
Correct Answer & Explanation
. Abductors and extensors
Explanation
In cerebral palsy, progressive hip subluxation and dislocation are driven by the muscle imbalance caused by spasticity. The spastic adductors and hip flexors (iliopsoas) overpower the relatively weaker abductors and extensors, driving the femoral head posteromedially and causing a progressive valgus and anteverted proximal femur, which leads to superolateral uncovering and eventual dislocation.
Question 4604
Topic: Pediatric Upper Extremity & Spine
A 4-year-old boy undergoes open reduction and internal fixation of a displaced Milch Type II lateral condyle fracture of the humerus. Which of the following is the most common complication associated with this injury and its treatment?
Correct Answer & Explanation
. Avascular necrosis of the trochlea
Explanation
Lateral spur formation, or lateral condylar overgrowth, is the most common complication of a lateral condyle fracture, occurring in up to 50-70% of cases. It causes a cosmetic bump on the lateral elbow but rarely restricts motion or causes functional deficits. While nonunion and tardy ulnar nerve palsy (due to cubitus valgus) are classic severe complications of a missed or poorly treated lateral condyle fracture, lateral overgrowth is far more frequent.
Question 4605
Topic: 4. Pediatrics
A 3-year-old girl with a BMI in the 98th percentile presents with bilateral severe bowing of the lower extremities. Radiographs reveal an abrupt varus angulation at the proximal tibial metaphysis with medial beaking. The metaphyseal-diaphyseal (Drennan) angle is 20 degrees. What is the most appropriate initial management?
Correct Answer & Explanation
. Bilateral knee-ankle-foot orthoses (KAFOs)
Explanation
The patient has infantile Blount's disease (tibia vara), characterized by medial metaphyseal beaking and a Drennan angle >16 degrees (which distinguishes it from physiologic bowing). For children under the age of 4 with Langenskiöld Stage I or II, bracing with KAFOs during weight-bearing hours is the standard initial treatment. Surgery (osteotomy) is indicated if bracing fails, or if the child is over age 4 at presentation.
Question 4606
Topic: Pediatric Hip
In Legg-Calvé-Perthes disease, which of the following clinical factors is considered the most significant prognostic factor for long-term hip joint survival and prevention of early osteoarthritis?
Correct Answer & Explanation
. Age at clinical presentation
Explanation
Age at clinical presentation is universally recognized as the most critical prognostic factor in Legg-Calvé-Perthes disease. Children who present at less than 6 to 8 years of age have a significant remodeling potential and generally fare better. Those over age 8 at presentation have a much higher rate of poor outcomes and early secondary osteoarthritis. The Lateral Pillar classification is the most significant radiographic prognostic factor.
Question 4607
Topic: 4. Pediatrics
A 13-year-old girl sustains an ankle injury while playing soccer. Radiographs demonstrate a Salter-Harris III fracture of the anterolateral distal tibia. Which of the following describes the mechanism of injury and the anatomic structure responsible for avulsing this fragment?
This is a juvenile Tillaux fracture, which is a Salter-Harris III fracture of the anterolateral distal tibial epiphysis. It occurs in adolescents due to the asymmetric closure of the distal tibial physis (central, then medial, then lateral). An external rotation force placed on the foot causes the strong Anterior Inferior Tibiofibular Ligament (AITFL) to avulse the unfused anterolateral epiphysis.
Question 4608
Topic: Pediatric Upper Extremity & Spine
A 12-year-old premenarchal female (Risser 0) presents with a right thoracic adolescent idiopathic scoliosis. Her curve measures 22 degrees on a standing PA radiograph. What is the approximate risk of curve progression to greater than 30 degrees?
Correct Answer & Explanation
. 10%
Explanation
According to the Lonstein and Carlson progression formula and established general guidelines for Adolescent Idiopathic Scoliosis, a patient who is highly immature (Risser 0-2, premenarchal) with a curve measuring between 20-29 degrees has approximately a 68% risk of curve progression. This warrants close observation or initiation of bracing.
Question 4609
Topic: 4. Pediatrics
A 5-year-old child with a history of multiple fractures, blue sclerae, and dentinogenesis imperfecta is diagnosed with Osteogenesis Imperfecta Type I. This condition is most commonly caused by a mutation in which of the following genes?
Correct Answer & Explanation
. FGFR3
Explanation
Osteogenesis Imperfecta (OI) is a genetic disorder of connective tissue primarily affecting Type I collagen. It is most commonly inherited in an autosomal dominant pattern and is caused by mutations in the COL1A1 or COL1A2 genes. FGFR3 is associated with achondroplasia; COMP with pseudoachondroplasia and multiple epiphyseal dysplasia; COL2A1 with spondyloepiphyseal dysplasia (SED); and RUNX2 with cleidocranial dysplasia.
Question 4610
Topic: Pediatric Hip
A 13-year-old boy presents to the emergency department unable to bear weight on his right leg after a minor fall 2 days ago. He has a history of vague right groin pain for 3 months. Radiographs demonstrate a severe, unstable slipped capital femoral epiphysis (SCFE). Which of the following best describes the rationale for performing a capsulotomy during surgical fixation?
Correct Answer & Explanation
. To assist with anatomic closed reduction
Explanation
Unstable SCFE (defined by the inability to bear weight) carries a high risk of avascular necrosis (AVN), reportedly up to 50%. The primary rationale for performing an anterior capsulotomy during surgical treatment of an unstable SCFE is to evacuate the fracture hematoma, thereby decompressing the joint and reducing intracapsular pressure, which theoretically improves perfusion to the femoral head and decreases the risk of AVN.
Question 4611
Topic: 4. Pediatrics
A 2-year-old boy presents with anterolateral bowing of the left tibia and a newly developed midshaft fracture. Radiographs reveal a narrowed, sclerotic medullary canal with a pseudarthrosis. This clinical presentation is most strongly associated with which of the following systemic conditions?
Correct Answer & Explanation
. Osteogenesis Imperfecta
Explanation
Congenital pseudarthrosis of the tibia (CPT) classically presents with anterolateral bowing of the tibia that fractures and fails to heal due to abnormal periosteum. It is strongly associated with Neurofibromatosis type 1 (NF1); approximately 50% of children with CPT have NF1. Conversely, posteromedial bowing is generally benign and resolves spontaneously.
Question 4612
Topic: Pediatric Hip
An 11-year-old girl with a body mass index (BMI) in the 99th percentile is diagnosed with a unilateral slipped capital femoral epiphysis (SCFE).
Which of the following is considered an absolute indication for prophylactic in situ pinning of the contralateral, asymptomatic hip?
Correct Answer & Explanation
. A modified Southwick angle greater than 50 degrees on the symptomatic side
Explanation
While factors such as young age, obesity, and open triradiate cartilage are relative indications that surgeons consider when discussing prophylactic pinning, the presence of an underlying endocrine or metabolic disorder (such as hypothyroidism, panhypopituitarism, or renal osteodystrophy) is universally considered an absolute indication for prophylactic pinning of the contralateral hip due to the extremely high risk of a subsequent slip.
Question 4613
Topic: 4. Pediatrics
A 3-and-a-half-year-old child presents with worsening bilateral genu varum. Radiographs demonstrate a prominent metaphyseal beak and depression of the medial proximal tibial physis consistent with Langenskiöld Stage III infantile Blount disease. What is the most appropriate management for this patient?
Correct Answer & Explanation
. Proximal tibial valgus osteotomy and concomitant fibular osteotomy
Explanation
Infantile Blount disease management is dependent on age and Langenskiöld stage. Bracing (KAFO) is generally indicated for children under 3 years old with Stage I or II disease. For a child over the age of 3 presenting with Stage III disease or higher, conservative management is unlikely to succeed. The standard of care is surgical realignment, typically through a proximal tibial valgus osteotomy combined with a fibular osteotomy to prevent recurrence and correct the mechanical axis.
Question 4614
Topic: Pediatric Upper Extremity & Spine
A 6-year-old boy falls from the monkey bars and sustains a Gartland Type III supracondylar humerus fracture. Upon initial evaluation, his hand is pale and pulseless. After prompt closed reduction and percutaneous pinning in the operating room, the hand becomes warm and pink, with a capillary refill of less than 2 seconds, but the radial pulse remains unpalpable. What is the next best step in management?
Correct Answer & Explanation
. Admit the patient for close inpatient observation and neurovascular monitoring
Explanation
The management of the 'pink, pulseless hand' following reduction of a supracondylar humerus fracture is a well-established algorithm. If the hand is well-perfused (pink, warm, good capillary refill) after adequate reduction and stabilization, collateral circulation is sufficient. The standard of care is to admit the patient for close neurovascular monitoring (observation) rather than pursuing immediate vascular exploration, as the brachial artery is often in spasm and recanalizes over time.
Question 4615
Topic: 4. Pediatrics
A 3-month-old infant is undergoing treatment for Developmental Dysplasia of the Hip (DDH) using a Pavlik harness. During a follow-up visit, the mother notes that the infant has stopped kicking the affected leg. On examination, the infant exhibits absent knee extension but normal ankle dorsiflexion and plantarflexion.
Which nerve injury is most likely, and what specific mechanical factor in the harness caused it?
Correct Answer & Explanation
. Femoral nerve palsy; caused by excessive hip flexion
Explanation
Femoral nerve palsy is the most common nerve injury associated with the use of a Pavlik harness for DDH. It is caused by excessive hip flexion, which tethers the femoral nerve against the inguinal ligament. The clinical presentation is an infant who stops kicking and loses active knee extension. Treatment consists of temporarily loosening or discontinuing the flexion straps or the harness entirely until function returns.
Question 4616
Topic: Pediatric Hip
An 8-year-old boy presents with a painful limp and limited hip abduction. Radiographs reveal fragmentation of the proximal femoral epiphysis with maintained height of the lateral pillar (>50% of original height), classifying it as Herring Lateral Pillar Group B Legg-Calvé-Perthes disease (LCPD). According to the multicenter prospective study by Herring et al., which intervention provides the best radiographic outcome for this specific patient profile?
Correct Answer & Explanation
. Surgical containment via a proximal femoral varus osteotomy or pelvic osteotomy
Explanation
According to the landmark multicenter prospective LCPD study by Herring et al., surgical containment (proximal femoral varus osteotomy or pelvic osteotomy) provides significantly better radiographic outcomes (Stulberg classification) compared to nonoperative treatment for children who are 8 years of age or older at the time of onset and who have Lateral Pillar Group B or B/C border disease.
Question 4617
Topic: 4. Pediatrics
A 6-year-old boy with spastic quadriplegic cerebral palsy (GMFCS level V) presents for routine hip surveillance. Anteroposterior pelvic radiograph reveals a Reimers migration percentage (migration index) of 45% in the right hip and 30% in the left hip. The patient experiences pain during diapering.
What is the most appropriate surgical management for the right hip?
Correct Answer & Explanation
. Adductor longus tenotomy alone
Explanation
In children with cerebral palsy, a Reimers migration percentage greater than 40-50% indicates significant subluxation with a high risk of progression to dislocation. Adductor tenotomy alone is generally reserved for lower migration indices (<30%) in younger patients. For a migration index of 45% in a 6-year-old, bony reconstruction utilizing a proximal femoral varus derotation osteotomy (VDRO) combined with a pelvic osteotomy (such as a Dega or Pemberton) is the gold standard to provide definitive coverage and containment.
Question 4618
Topic: Pediatric Lower Extremity
An orthopaedic surgeon is treating a newborn with an idiopathic clubfoot using the Ponseti method of serial casting.
Which of the following describes the correct sequential order of deformity correction using this technique?
Correct Answer & Explanation
. Equinus, Varus, Adductus, Cavus
Explanation
The Ponseti method dictates a very specific sequential correction of the clubfoot deformities, remembered by the acronym CAVE: 1) Cavus (corrected by supinating the forefoot to align it with the hindfoot), 2) Adductus, 3) Varus (corrected simultaneously by abducting the foot around the talar head), and finally 4) Equinus (often requiring a percutaneous Achilles tenotomy once the heel is in valgus or neutral).
Question 4619
Topic: Pediatric Lower Extremity
A newborn is evaluated for a congenital limb deficiency. Clinical examination and radiographs demonstrate an absent lateral malleolus, a shortened tibia, absent lateral rays of the foot, and marked anteromedial bowing of the tibia.
Which of the following internal knee derangements is nearly universally associated with this condition?
Correct Answer & Explanation
. Anterior cruciate ligament (ACL) deficiency
Explanation
The clinical picture describes fibular hemimelia (longitudinal deficiency of the fibula). It is well established that fibular hemimelia is a spectrum that affects the entire limb. A nearly universal association with fibular hemimelia is the absence or severe deficiency of the anterior cruciate ligament (ACL). Other common associations include a ball-and-socket ankle joint, tarsal coalitions, and absence of the lateral rays of the foot.
Question 4620
Topic: 4. Pediatrics
A 2-month-old infant is brought to the clinic due to a consistent head posture. The mother notes the baby's head is tilted toward the right shoulder, and the chin is rotated toward the left. On examination, a firm, non-tender, olive-shaped mass is palpable in the lower third of the right sternocleidomastoid muscle.
What is the most appropriate initial management for this condition?
Correct Answer & Explanation
. Immediate MRI of the cervical spine to rule out congenital vertebral anomalies
Explanation
The clinical presentation is classic for Congenital Muscular Torticollis (CMT) with an SCM pseudo-tumor (fibromatosis colli). The initial management for CMT is conservative, consisting of a physical therapy program emphasizing gentle, sustained passive stretching of the affected sternocleidomastoid muscle, as well as positioning techniques. This resolves the condition in over 90% of cases if initiated early (<1 year of age). Surgical release is reserved for recalcitrant cases persisting beyond 12-18 months of age.
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