Question 1281
Topic: Pediatric HipIn addition to the short and thick tubular bones seen in the radiograph below, what other skeletal anomaly is frequently associated with this syndrome?
Correct Answer & Explanation
. Absence of clavicles
Practice Set 65 of 104
This practice set contains high-yield board review questions covering key concepts in Pediatric Hip. Each clinical scenario is designed to test your diagnostic and management skills relevant to this subspecialty.
In addition to the short and thick tubular bones seen in the radiograph below, what other skeletal anomaly is frequently associated with this syndrome?
. Absence of clavicles
A 12-year-old girl with end-stage renal disease presents with bilateral hip pain. Radiographs demonstrate a "rugger jersey" spine and a slipped capital femoral epiphysis. Her PTH is markedly elevated. What is the primary mechanism driving her skeletal disease?
. Phosphate retention and decreased calcitriol production
A 10-year-old girl with cleidocranial dysplasia presents with a progressively waddling gait.
Based on the typical pelvic pathology of this condition, what is the most likely diagnosis?
. Coxa vara
A 9-year-old girl with cleidocranial dysplasia presents for follow-up.
She has bilateral coxa vara with a neck-shaft angle of 95 degrees and a Hilgenreiner epiphyseal angle (HEA) of 65 degrees. What is the most appropriate management for her hips?
. Valgus-producing proximal femoral osteotomies
A 7-year-old girl is evaluated for delayed eruption of secondary dentition and an unusual ability to appose her shoulders anteriorly. Radiographs confirm absent clavicles.
Which of the following orthopaedic manifestations is most commonly associated with this genetic syndrome?

. Coxa vara
A 2-week-old neonate presents with pseudoparalysis of the right lower extremity and crying upon diaper changes. Ultrasound confirms a significant hip effusion.
What is the most appropriate next step in management?
. Immediate joint aspiration, arthrotomy, and irrigation
A 3-week-old neonate presents with fever, irritability, and a pseudoparalysis of the right lower extremity. Ultrasound reveals a hip joint effusion.
What is the most appropriate next step in management?
. Urgent hip aspiration and surgical drainage
A 3-week-old neonate presents with pseudoparalysis of the right leg and crying with diaper changes. There is no fever, but CRP is significantly elevated. Ultrasound reveals a hip effusion. If this neonatal septic arthritis (coxitis) is diagnosed late and untreated, what is the most severe classical long-term orthopedic complication?
. Resorption of the femoral head and neck (Tom Smith arthritis)
A 12-year-old obese boy presents with a left slipped capital femoral epiphysis (SCFE). Which of the following is an absolute indication for prophylactic in situ pinning of the contralateral, asymptomatic hip?
. Presence of an underlying endocrine disorder
. Early fragmentation stage
A 45-year-old female with Crowe IV developmental dysplasia of the hip (DDH) is undergoing a total hip arthroplasty. The surgeon plans to place the acetabular component at the true anatomic hip center and perform a subtrochanteric shortening osteotomy. Which of the following is the primary rationale for performing the shortening osteotomy in this specific scenario?
. To prevent sciatic nerve palsy
A 40-year-old female with severe unilateral developmental dysplasia of the hip (Crowe type IV) undergoes a complex THA requiring significant leg lengthening. Postoperatively, she is unable to actively dorsiflex her foot or extend her great toe, and has numbness over the dorsum of her foot. What is the most common intraoperative mechanism for this specific neurologic complication?
. Excessive limb lengthening causing stretch injury to the peroneal division of the sciatic nerve
. Subtrochanteric shortening osteotomy
A 40-year-old female with Crowe IV developmental dysplasia of the hip is undergoing a total hip arthroplasty. The surgeon plans to place the acetabular component at the level of the true anatomic acetabulum. What additional procedural step is most likely required to safely accomplish this reduction?
. Subtrochanteric shortening osteotomy
A newborn with Down syndrome undergoes a pelvic radiograph for hip screening. Which of the following classic radiographic findings is typically seen in the pelvis of infants with Trisomy 21?
. Decreased iliac index with flattened acetabular roofs and flared iliac wings
A 10-year-old male with Down syndrome presents with a 3-week history of a limp and poorly localized knee pain. Radiographs confirm a slipped capital femoral epiphysis (SCFE). Compared to an idiopathic SCFE in a neurotypical child, this patient is at an increased risk for which of the following?
. Bilateral involvement
. Slipped capital femoral epiphysis (SCFE)
. Symmetric, bilateral involvement and autosomal dominant inheritance favor MED
A 2-week-old neonate presents with asymmetric hip creases, fever, and pseudoparalysis of the right lower extremity. Ultrasound confirms a large hip effusion, and emergent surgical drainage is performed. The clinical image below demonstrates severe sequelae of a missed diagnosis in a similar patient.
What is the most devastating long-term complication of delayed diagnosis of neonatal septic arthritis of the hip?
. Complete avascular destruction of the femoral head and neck with hip subluxation
. Multiple epiphyseal dysplasia