Orthopaedic oncology Structured oral examination question 2: Enchondroma

Orthopaedic oncology Structured oral examination question 2: Enchondroma

Figure 7.2 Enchondroma.

EXAMINER: Tell me about these radiographs of this chaps right foot. (Figure 7.2.)

CANDIDATE: Well theyre AP and oblique views and they

show an expansile, lytic lesion in the proximal phalanx of his second toe.

EXAMINER: What do you think it is?

CANDIDATE: The radiographs show features consistent with an enchondroma. It has a short zone of transition and appears quite well defined. Theres also some stippled calcification within the substance of the lesion, which suggests a chondroid matrix.

 

 

 

EXAMINER: How would you treat this lesion?

CANDIDATE: Well, I would want to get more information so

I would take a full history and examination. I would also want to get more imaging of the lesion with an MRI and discuss the pictures with a bone tumour MDT. If theres any doubt about the diagnosis they may want to do a biopsy, but in general the surgical treatment of an enchondroma is with curettage, with or without grafting.

General advice: Even if the diagnosis appears obvious and is of a benign lesion, dont be rushed into offering surgical treatment. Always work through history, examination and imaging. You will never be criticized for discussing the diagnosis with a bone tumour MDT, but you will end up in a very tricky discussion with the examiners and fail if you have made the wrong diagnosis, it turns out to be malignant, and youve not discussed it with an MDT first.

Other points:

 

50% of solitary enchondromas arise in the hands. Malignant transformation is very rare, but when it does occur it is usually in large lesions of long bones.

 

Enchondromatosis = Olliers disease (risk of bone malignancy is 10%, but if visceral and

 

 

 

brain malignancies are included then the overall risk is 25%).

 

Enchondromatosis + haemangiomas = Maffucci syndrome (risk of malignancy approaching 100%).